A cause of the crimping sine syndrome is frequently nonspecific scarred degeneration in the excitation line system of the heart or a mechanical overstretching of the forecourts. With children it is often observed after operations within the range of the right forecourt in the case of innate heart errors, in particular after the Fontan operation (which however with increasing experience decreases).

Definition and use of the term

A generally accepted definition of the crimping sine syndrome does not exist. Theoretically the diagnosis can be placed, if at least one of the typical findings in the electrocardiogram were proven:

• sine bradycardia without other cause,
• Sine knot stop,
• sinuatrialer block,
• Forecourt flares,
• Forecourt-flutter and
• tachycardias.

Since these rhythm disturbances ranking among the syndrome are however differently treated, their designation with the common term crimping sine syndrome is uncommon. The term becomes related usually only under special circumstances, in particular

1. minted with the combined occurrence of rhythm disturbances with low and high pulse frequencies (tachycardia bradycardia syndrome) and
2. for traditional reasons for the reason of a cardiac pacemaker therapy with sine bradycardia, sine knot stop or sinuatrialem block.

Organization according to kind of the rhythm disturbance

• Sine detention
• SA block
• Sine bradycardia
• of extra impacts
• tachycardia
• Forecourt flares
• Forecourt-flutter
• Bradycardia tachycardia syndrome

Causes

The most frequent cause of the crimping sine syndrome is probably the arterial high pressure, which leads to a chronic pressure load of the forecourts and then also to overstretching the muscle fibers.

Further causes are:

• SSS without recognizable structural heart illness
• with myocarditis
• with intoxications
• during forecourt overstretching
• during hypertensiver heart illness
• with Mitralklappenfehlern
• with Trikuspidalklappenfehlern.
• with pulmonalem high pressure
• with Perikarditis konstriktiva
• during koronarer heart illness
  • with blood circulation disturbance of the sine knot and the forecourt
  • without blood circulation disturbance of the sine knot and the forecourt

Investigation possibilities

The crucial research method for the recognition of the crimping sine syndrome is the long-term electrocardiogram. Also a Echokardiografie.Seltener is meaningful is necessarily a load electrocardiogram, a long-term blood pressure measurement or Herzkatheteruntersuchung.Eine special, very complex research method of the crimping sine syndrome is the electricalphysiological investigation.

Therapy

Apart from the treatment of the basic illness the following medicines worked satisfactorily:

• Beta blocker,
• Amiodaron

If an enlargement of the forecourt is provable and is present forecourt flares, an anti-coagulation should be introduced. (S. Cumarine) with bradycardiac forms of the crimping sine syndrome the implantation of a cardiac pacemaker is meaningful. A catheter ablation is accomplished only rarely so far with the crimping sine syndrome.

Literature

• Adan V, Crown LA: Diagnosis and Treatment OF crimp sine of syndromes (2003) at the Fam Physician 67:1725 - 32.

Web left

• HerzKinderWiki - for parents of heart-ill children with innate heart error, with meeting, left, literature and association lists

Articles in category "Crimping sine syndrome"

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