Total (TAPVC)

All four Lungenvenen are attached at right cycle. A complete is thus present. They can flow into different portions:

• the upper and/or lower Hohlvene
• right forecourt
• the Lebervene

An operation is accomplished as as possible immediately after the diagnosis under employment of a heart lung machine. If the Foramen oval locks after the birth too fast, as bypass up to the operation a Rashkind maneuver (to tear the forecourt septum) is implemented.

Partial

Only one part of the Lungenvenen flows wrongly and it concerns only in each case one lung, whereby the false delta of the right Lungenvenen seems twice as frequently like those to the left. They flow into

• the upper Hohlvene
• in right forecourt
• rarely into the lower Hohlvene additionally an atrium septum defect (ASD) is in most cases present.

By the partial wrong delta of the Lungenvenen arrived oxygen-rich blood increases to the right and loads volume-moderately the right heart (forecourt and Herzkammer) and leads to increased Lungendurchblutung.Die of children is usually fully loadable and free and. The heart error is discovered often coincidentally in the context of a preventive medical examination or a Infektes.

If a clear load of the right heart and the lung is present, the operation under employment is indicated to the heart lung machine. The misdirected lung blood is rerouted by means of a Patches in tunnel form into the left forecourt.

The Scimitar syndrome

A very rare form of a partial is the Scimitar syndrome. All or a part of the Lungenvenen from the right lung - mostly the Lungenvenen of the right central and Unterlappens - flow into a collecting container, which pulls to the lower Hohlvene in the area of the Zwerchfells and flows there. This collecting container is to be recognized in the radiograph. It has a wound process, which reminds of the form of a Turkish sword - a Scimitars -. This designation was used for the first time 1956. There are however already descriptions of this disease picture from the years 1836 and 1912. Also blood vessels can pull from the Aorta to this lung rags and thus lung areas form, which are flooded with blood. These portions are called Lungensequester. Frequently the right lung and/or the bronchi are underdeveloped and shifted the heart on the right side with this disease picture. The high blood supply to the right heart (left-right-shunted) leads to a load of the entire heart achievement and the lung and can lead to increased lung infections and bronchitides. Particularly during an additional blood supply from the Aorta is a increased risk for a Pulmonale hypertonia (lung high pressure). One differentiates between a "“adult form"” of this disease picture, which becomes as apparent with the atrium septum defect in form of a Shunts by the "“infant form"”, with which a heavy underdevelopment of the lung is present and a Pulmonale hypertonia developed. The treatment of the Scimitar syndrome exists in a surgical correction. The blood river from the Scimitar Vene is rerouted by means of Patch techniques into the left heart pre-chamber. The procedure depends on the anatomical findings of the patient. The long-term results with the adult form after the operation are favorable as to regard. With the infant form the prognosis depends on the extent of the lung participation.

Diagnostics

• in the electrocardiogram (ELECTROCARDIOGRAM) is a right heart load
• the Echokardiografie shows an increased right Herzkammer and an extended Pulmonalstamm
• in the radiograph one recognizes (easy) a heart enlargement and increased lung blood circulation
• the heart catheter investigation is necessary for the exact representation of the Lungenvenen and their muzzle place

Long-term expectations

Long-term successes after the operation of a are usually very good. Up to (possibly) the "“infant form"” with the Scimitar syndrome are to be expected no restriction of the maximum stress. Lifelong kardiologische control investigations in larger distances are indicated. Also on the lifelong Endokarditisprophylaxe must be respected.

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Articles in category "Lungenvenenfehlmng"

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